致心律失常性右室心肌病论文

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1、致心律失常性右室心肌病论文致心律失常性右室心肌病(arrhythmogenicrightventricularcardiomyopathy,ARVC)是一种原因不明的心肌疾病,病变主要累及右室(RV),以RV心肌不同程度地被脂肪或纤维脂肪组织代替为特征。临床主要表现为室性心律失常或猝死,但亦可无症状［1～4］。生前不易作出临床诊断。近20年来,国外对本病的研究取得了较大进展,在国内也日益受到重视。1.ARVC的概念ARVC在文献中曾被称为羊皮纸心、Uhl氏畸形、RV脂肪浸润或脂肪过多症、RV发育不良、致心律失常性右室发育不良(AR

2、VD)、RV心肌病、ARVC,以后三种使用较广泛,法国学者多使用“ARVD”,意大利学者多使用“ARVC”。文献中,一些ARVC常被描述为Uhl畸形,两者须加以鉴别。Uhl畸形是真性先天畸形，为先天性RV肌完全缺如,心室壁薄如纸,.freelyopathyandsuddendeathinyoungpeople.NeontiB,Sinagra,G,LenardaAD,etal.Leftventricularinvolvementinrightventricularcardiomyopathy.PostgradMedJ,1992,68

3、(suppl1):S36-S39.［3］KerenA,PoppRL.Assignmentofpatientsintotheclassificationofcardiomyopathies.Circulation,1992,86:1622-1633.［4］MenghettiL,BassoC,NavaA,etal.Spin-echonuclearmagicresonancefortissuecharacterisationinarrhythmogenicrightventricularcardiomyopathy.BrHeartJ,1

4、996,76:467-470.［5］PinamontiB,SinagraG,SalviA,etal.Leftventricularinvolovementinrightventriculardysplasia.AmHeartJ,1992,123:711-724.［6］GerlisLM,Schmidt-OttSC,HoSY,etal.Dysplasticconditionoftherightventricularmyocardium:Uhlsanormalyarrhythmogenicrightventriculardysplas

5、ia.BrHeartJ,1993,69:142-150.［7］张兆祥,张美文,黄利鸣.右心室心肌病猝死——五例病理尸检观查.中国循环杂志,1995,10:291-293.［8］BassoC,ThieneG,CorradoD,etal.Arrhythmogenicrightventricularcardiomyopathy.Dysplasia,dystrophy,ormyocarditis?Circulation,1996,94:983-991.［9］秦启生,SteinbachTH.脂肪心的形态学,形态测量学及心肌脂肪含量测定.中国

6、法医学杂志,1988,3:20-23.［10］RossiMA,BrazilRP.parisonofChagasheartdiseasetoarrhythmogenicrightventricularcardiomyopathy.AmHeartJ,1995,129:626-629.［11］BujaG,NavaA,DalientoL,etal.RightventricularcardiomyopathyinidenticalandnonidenticalyoungtHeartJ,1993,126:1187-1193.［12］Mcla

7、yJS,NorrisA,CampbellRarcusFI,FontaineGH,GuiraudonG,etal.Rightventriculardysplasia:Areportof24adultcases.Circulation,1982,65:384-398.［16］CorradoD,ThieneG,NavaA,etal.Suddendeathinyoungpetitiveathletes:clinicopathologiccorrelationsin22cases.AmJMed,1990,89:588-596.［17］Mia

8、niD,PinamontiB,BussaniR,etal.Rightventriculardysplasia:aclinicalandpathologicalstudyoftiliesent.BrHeartJ,1993,69:151-157.［18