肾脏局灶性囊性病变2011课件

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1、LocalizedCysticDiseaseoftheKidney肾脏局灶性囊性病变IntroductionLocalizedcysticdiseaseofthekidneyisabenignnonsurgicalcondition.肾局灶囊性病变是一种良性的非手术治疗的肾脏疾病Itsimagingandclinicalfeaturesarecharacterizedanddifferentiatedfromautosomaldominantpolycystickidneydisease,multilocularcysticnephroma,andcysticneoplasm.它的影像学和

2、临床特征与常染色体显性遗传性多囊肾病、多房性囊性肾脏肿瘤、肾脏肿瘤囊变有区别IntroductionLocalizedcysticdiseaseofthekidneyhasbeenreferredtobyanumberofdifferentnames,includingsegmentalcysticdiseaseofthekidneywhenitinvolvesjustoneportionofonekidney,orunilateralcysticdiseaseofthekidneywhenitinvolvesallofonekidney.肾脏局灶性囊性病变有不同的名称，包含肾的阶段性囊肿

3、性病变（它累及一个肾的某一部分），或者肾脏的单侧囊性病变（累及一个肾脏的全部）IntroductionIthasalsobeenreferredtoas“unilateralpolycysticdisease”.Thelattertermmaybemisleadingandshouldbediscardedbecausethislesionbearsnorelationshiptoautosomaldominantpolycystickidneydisease,whichisafamilialdiseasewithavarietyofassociatedconditions，noneofw

4、hichareseeninlocalizedcysticdisease.它亦指单侧的先天性多囊肾，但后者术语可能被误解,应该抛弃,因为这种病变与常染色体显性遗传性多囊肾并没有关系,后者是一个家族性疾病，有各种各样的相关条件，几乎没有一个表现为肾脏局灶性囊性病变。IntroductionLocalizedcysticdiseasewasunilateralinallpatientsandcharacterizedbymultiplecystsofvarioussizesseparatedbynormal(oratrophic)renaltissueinaconglomeratemasssug

5、gestiveofcysticneoplasm若病变单侧发病，在团块状肿块内出现不同尺寸的多发囊肿被正常（或萎缩）的肾组织分隔多提示为囊性肿瘤Clinicalpresentationsincludedhematuria,flankpain,palpableabdominalmass,andlocalizedcysticdiseaseasanincidentalfinding临床表现包括血尿,腹痛、可触及的腹部肿块和偶然发现局部囊性病变Noneofthepatientshadafamilyhistoryofautosomaldominantpolycystickidneydisease.所有

6、的病人均无常染色体显性遗传性多囊肾病的家族史Familiaritywithlocalizedcysticdiseaseofthekidneyanditsimagingfindingsisimportanttoavoidunnecessarysurgeryandtodifferentiatethediseasefromautosomaldominantpolycystickidneydisease熟悉肾脏的局部囊性疾病和它的影像学表现是重要的,以避免不必要的外科手术，并且和常染色体显性遗传性多囊肾相区别IntroductionIntroductionCysticdiseasesoftheki

7、dneyencompassawidespectrumofcauses,manifestations,andtreatments肾脏囊性病变的病因、临床表现与治疗各不相同Localizedcysticdiseaseisanuncommonpresentationofrenalcysticdiseaseandhasbeenconfusedwithunilateralautosomaldominantpolycystickid